Caring for Pediatric Patients with Epidermolysis Bullosa in the Emergency Department

Helena A. Jenkinson, Ashley D. Lundgren, Moise L. Levy, Lucia Z. Diaz

Research output: Contribution to journalReview article

Abstract

Epidermolysis bullosa (EB) refers to a heterogeneous group of genetic disorders characterized by epithelial fragility. We provide guidelines for management of pediatric patients with EB in the emergency department based on a review of literature, as well as insights from our own experiences caring for patients with EB. The purpose of the guidelines proposed is prevention of avoidable iatrogenic trauma to the skin and mucosa of patients with EB who are presenting to the emergency department for a variety of reasons.

Original languageEnglish (US)
Pages (from-to)579-584
Number of pages6
JournalPediatric Emergency Care
Volume35
Issue number8
DOIs
StatePublished - Aug 1 2019

Fingerprint

Epidermolysis Bullosa
Hospital Emergency Service
Pediatrics
Guidelines
Inborn Genetic Diseases
Mucous Membrane
Skin
Wounds and Injuries

Keywords

  • epidermolysis bullosa
  • health care delivery
  • iatrogenic trauma
  • immunobullous disease
  • mucosa
  • skin
  • wound care

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Emergency Medicine

Cite this

Caring for Pediatric Patients with Epidermolysis Bullosa in the Emergency Department. / Jenkinson, Helena A.; Lundgren, Ashley D.; Levy, Moise L.; Diaz, Lucia Z.

In: Pediatric Emergency Care, Vol. 35, No. 8, 01.08.2019, p. 579-584.

Research output: Contribution to journalReview article

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